Lipoid proteinosis presenting with neuropsychiatric manifestations.
Journal of Neurology Neurosurgery & PsychiatryPublished 1 December 1985Open access
Richard Emsley, L Paster
Citations45
SJR quartileQ1
SJR score3.38
SNIP2.41
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TL;DR
Two patients with lipoid proteinosis reported in whom paranoid symptoms were the presenting feature had a long standing impairment of memory and bilateral medial temporal lobe calcification demonstrated by CT scan.
Abstract
Two patients with lipoid proteinosis are reported in whom paranoid symptoms were the presenting feature. Both had a long standing impairment of memory and bilateral medial temporal lobe calcification demonstrated by CT scan. Possible associations between the anatomical site of these lesions and the neuropsychiatric manifestations are discussed.
Keywords
Medicine
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QJMLipoid Proteinosis; a clinical, pathological and genetic study
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