A new variant of Creutzfeldt-Jakob disease in the UK
The LancetPublished 1 April 1996
Robert Will, James W. Ironside, Martin Zeidler, K. Estibeiro, Simon Cousens, Peter G. Smith
Citations2,698
SJR quartileQ1
SJR score12.11
SNIP22.72
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TL;DR
Ten cases of Creutzfeldt-Jakob disease have been identified in the UK in recent months with a new neuropathological profile that raises the possibility that they are causally linked to BSE.
Abstract
These cases appear to represent a new variant of CJD, which may be unique to the UK. This raises the possibility that they are causally linked to BSE. Although this may be the most plausible explanation for this cluster of cases, a link with BSE cannot be confirmed on the basis of this evidence alone. It is essential to obtain further information on the current and past clinical and neuropathological profiles of CJD in the UK and elsewhere.
Keywords
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