Classification of the cardiomyopathies: a position statement from the european society of cardiology working group on myocardial and pericardial diseases
European Heart JournalPublished 5 October 2007Open access
Perry Elliott, B. Andersson, Eloisa Arbustini, Zofia T. Bilińska, Franco Cecchi, Philippe Charron
Citations2,998
SJR quartileQ1
SJR score4.99
SNIP8.87
Generate an AI Snapshot to get a quick, structured summary of this paper.
Study Snapshot
ObjectiveStudy objective
MethodsResearch methodology
PopulationPopulation studied
Sample sizeSample sizes
OutcomesStudy outcomes here
ResultsStudy results comes here
LimitationsResearch study limitations comes here
A concise AI-generated summary of the paper will appear here once you click Generate AI Snapshot.
TL;DR
This document, The European Society of Cardiology Working Group on Myocardial and Pericardial Diseases presents an update of the existing classification scheme, to help clinicians look beyond generic diagnostic labels in order to reach more specific diagnoses.
Abstract
In biology, classification systems are used to promote understanding and systematic discussion through the use of logical groups and hierarchies. In clinical medicine, similar principles are used to standardise the nomenclature of disease. For more than three decades, heart muscle diseases have been classified into primary or idiopathic myocardial diseases (cardiomyopathies) and secondary disorders that have similar morphological appearances, but which are caused by an identifiable pathology such as coronary artery disease or myocardial infiltration (specific heart muscle diseases). In this document, The European Society of Cardiology Working Group on Myocardial and Pericardial Diseases presents an update of the existing classification scheme. The aim is to help clinicians look beyond generic diagnostic labels in order to reach more specific diagnoses.
Keywords
Medicine
CirculationContemporary Definitions and Classification of the Cardiomyopathies
3,411 Citations2006Barry J. Maron, Jeffrey A. Towbin +7 more
The present classification scheme recognizes the rapid evolution of molecular genetics in cardiology, as well as the introduction of several recently described diseases, and is unique in that it incorporates ion channelopathies as a primary cardiomyopathy.
HeartDiagnosis of arrhythmogenic right ventricular dysplasia/cardiomyopathy. Task Force of the Working Group Myocardial and Pericardial Disease of the European Society of Cardiology and of the Scientific Council on Cardiomyopathies of the International Society and Federation of Cardiology.
1,647 Citations1994William J. McKenna, Gaetano Thiene +5 more
Diagnosis of arrhythmogenic right ventricular dysplasia/cardiomyopathy is confirmed with positive results for both EMT and CT scan.
European Heart JournalApical ballooning syndrome or takotsubo cardiomyopathy: a systematic review
1,488 Citations2006Monica Gianni, Francesco Dentali +4 more
Clinicians should consider this syndrome in the differential diagnosis of patients presenting with chest pain, especially in post-menopausal women with a recent history of emotional or physical stress.
New England Journal of MedicineIdiopathic Dilated Cardiomyopathy
970 Citations1994G. William Dec, Valentı́n Fuster
European Heart JournalAmerican College of Cardiology/European Society of Cardiology Clinical Expert Consensus Document on Hypertrophic Cardiomyopathy A report of the American College of Cardiology Foundation Task Force on Clinical Expert Consensus Documents and the European Society of Cardiology Committee for Practice Guidelines
699 Citations2003Barry J. Maron
The reader should view the CECD as the best attempt of the ACC and the ESC to inform and guide clinical practice in areas where rigorous evidence may not yet be available or the evidence to date is not widely accepted.
CirculationPregnancy-Associated Cardiomyopathy
532 Citations2005Uri Elkayam, Mohammed W. Akhter +5 more
Clinical presentation and outcome of patients with pregnancy-associated cardiomyopathy diagnosed early in pregnancy are similar to those of Patients with traditional peripartum cardiopathy, suggesting these 2 conditions may represent a continuum of a spectrum of the same disease.
Journal of the American College of CardiologyClinical and genetic issues in familial dilated cardiomyopathy
485 Citations2005Emily Burkett, Ray E. Hershberger
Echocardiographic and electrocardiographic screening of first-degree relatives of individuals with IDC and FDC is indicated, as detection and treatment are possible before the onset of advanced symptomatic disease.
European Heart JournalGuidelines for the study of familial dilated cardiomyopathies
449 Citations1999Luisa Mestroni
Current Treatment Options in Cardiovascular MedicineHypertrophic Cardiomyopathy
409 Citations2002Elijah R. Behr, William J. McKenna
All patients with HCM should be assessed for their risk of sudden death regardless of severity of symptoms or morphology, and the threshold for initiation of anticoagulation should be low in patients with sustained palpitations, atrial enlargement, and nonsustained supraventricular arrhythmia on Holter.
CirculationClinical Features and Outcomes of Childhood Dilated Cardiomyopathy
379 Citations2006Piers E.F. Daubeney, Alan Nugent +7 more
Early mortality is high in childhood dilated cardiomyopathy, but the clinical status of long-term survivors is good, and this population-based study identifies children at risk of adverse events.
HeartIsolated ventricular non-compaction of the myocardium in adults
312 Citations2006Rolf Jenni, Erwin Oechslin +1 more
Isolated ventricular non-compaction in adults is a genetic cardiac disease of emerging importance with a distinct clinical and pathophysiological presentation.
HeartThe frontiers of cardiomyopathy.
250 Citations1982J. F. Goodwin
It is suggested that no longer are the cardiomyopathies rare or curious diseases but relatively common disorders which are of interest to medical scientists in many fields and no longer the sole problem of the cardiologist.
CirculationClinical Features and Outcomes of Childhood Hypertrophic Cardiomyopathy
195 Citations2005Alan Nugent, Piers E.F. Daubeney +7 more
Syndromal, genetic, and metabolic causes predominate in children with hypertrophic cardiomyopathy; Ventricular outflow tract obstruction is common and the clinical status of long-term survivors is good.
European Heart JournalCardiomyopathies: is it time for a molecular classification?
101 Citations2004Gaetano Thiene, Domenico Corrado +1 more
According to the new definition of cardiomyopathies as diseases of the myocardium associated with cardiac dysfunction, they should include not only forms with depressed contractility and impaired diastolic function, but also conduction and rhythm disturbances and enhanced arrhythmogenicity.
CirculationMildly dilated congestive cardiomyopathy.
94 Citations1985Andre Keren, M E Billingham +3 more
It is concluded that end-stage congestive cardiomyopathy may occur without significant ventricular dilatation and patients with MDCM have heart sizes intermediate between those found in IRCM and DCM but their clinical, hemodynamic, and pathologic findings are virtually identical to those of patients with typical DCM.
CirculationMildly dilated congestive cardiomyopathy. Use of prospective diagnostic criteria and description of the clinical course without heart transplantation.
81 Citations1990Andre Keren, Shmuel Gottlieb +5 more
Heart transplantation should be strongly considered in MDCM if signs of severe cardiac dysfunction persist despite therapy, with poor survival in patients with persistence of the original diagnostic features during follow-up.