Proposed Diagnostic Criteria for the Brugada Syndrome
European Heart JournalPublished 1 November 2002
Arthur A.M. Wilde
Citations328
SJR quartileQ1
SJR score4.99
SNIP8.87
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TL;DR
In regions of Southeast Asia where it is endemic, the clinical presentation of Brugada syndrome is distinguished by a male predominance and the appearance of arrhythmic events at an average age of 40 years.
Abstract
(see 3,4 for review). TheBrugada syndrome is a familial disease displaying anautosomal dominant mode of transmission with incom-plete penetrance and an incidence ranging between 5 and66 per 10 000. In regions of Southeast Asia where it isendemic, the clinical presentation of Brugada syndromeis distinguished by a male predominance (8:1 ratio ofmales:females) and the appearance of arrhythmic eventsat an average age of 40 years (range: 1 to 77 years)
Keywords
MedicineBiochemistry, Genetics and Molecular Biology
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